Case Report

Anaesthetic considerations in a child with fibrodysplasia ossificans progressiva

DOI: 10.1080/22201181.2018.1517918
Author(s): Thomas KleyenstüberDepartment of Anaesthesia, Rahima Moosa Mother and Child Hospital, South Africa

Abstract

Fibrodysplasia ossificans progressiva (FOP) is an extremely rare genetic disorder characterised by extraskeletal ossification of connective tissue. Affected individuals often become completely immobilised by their third decade of life. Amongst numerous anaesthetic concerns, the airway management of patients with FOP may prove to be the greatest challenge. This case report describes the anaesthetic management of a three-year-old girl with FOP and highlights the difficulties encountered during airway management.

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