Idiopathic acquired progressive left facial hemiatrophy (Parry-Romberg syndrome) in a 21-year-old man in semi-urban, south-west Nigeria

Abstract

Idiopathic progressive hemifacial atrophy, or Parry-Romberg syndrome, is a rare entity, seldom described in medical texts. Though first described in 1825, as yet there are no clear-cut diagnostic criteria. It is of interest mainly because of the numerous features with which it may be associated, which are largely in the central nervous system, and, more importantly, because it can easily be confused with localised scleroderma en coup de sabre.